Online ISSN: 1303-6289
Print ISSN: 0304-4793


Published Online: 
April 18, 2005


 

Turkish Archives of Otolaryngology 2005; 43(1): 32-36 Abstract




Full Text in Turkish [PDF] 399 KB


 

 

 

 

Aggressive Infantile Fibromatosis: A Case Report

Agresif İnfantil Fibromatosis: Olgu Sunumu

G. Eker Uluçay, M. Akan, V. Kadılar, T. Aköz


Dr. Lütfi Kırdar Training and Research Hospital, Clinics of Plastic and Reconstructive Surgery, Istanbul, Turkey
Key Words

Aggressive infantile fibromatosis, recurrence, metastasis

Abstract

 

 

 

Aggressive infantile fibromatosis encountered in infants and in childhood is an aggressive, infiltrating, non-metastasizing disease characterized by a benign neoplastic histology and has a tendency to recur locally when not excised adequately. Because of local aggressiveness and a high rate of recurrence, wide local excision must be performed by careful dissection preserving major vital structures. The role of radiotherapy in aggressive infantile fibromatosis has not been established, but cases of tumor regression have been observed with chemotherapy. A one-year-old boy was presented to our clinic with a congenital history of a mass in the left neck region. A fine-needle aspiration biopsy was performed when he was 3 months old in another institution and the result was fibromatosis histologically. In our clinic we performed ultrasonography and computerized tomography. The result of ultrasonography demonstrated that the mass was 6.5x7x5 centimeter and there were multiple lymphadenopathies greater than 1.5 centimeter in jugular chain and in posterior cervical region. In CT of the cervical region a heterogenic mass that originated from the sternocleidomastoid muscle was measured as 9x8x8 centimeter and it displaced the larynx to the right side. The mass was excised totally and there was no recurrence in two years follow-up period. Aggressive infantile fibromatosis must be always kept in mind in the differential diagnosis in infants and children that present with a cervical mass.

Accepted after revision:  July 6, 2004
Correspondence:
Güniz Eker Uluçay, MD 
Emanet Sok. Sema Apt. No: 9 D: 10, Bostancı, İstanbul - Türkiye
Phone: (0216) 416 86 88
e-mail:
gunizeker@yahoo.com  

   
   


Copyright © 2005 by the Turkish Otolaryngology & Head and Neck Surgery Foundation.